https://www.google.com/search?q=cystic+fibrosis+life+expectancy+over+time&sxsrf=ALeKk016cqLMKFOIN13Mo-zeZNVPSE2UZA:1582124896557&tbm=isch&source=iu&ictx=1&fir=Z8PqiB9wE9aA7M%253A%252CqIc1hAFcgrcf6M%252C_&vet=1&usg=AI4_-kQiOMvWOmQo3nSft_g6pelUIPndYw&sa=X&ved=2ahUKEwio_8vD8t3nAhUjO30KHUm6DsAQ9QEwAHoECAcQAw#imgrc=xYxJSwiLz6lK5M
药物可以到达肺泡,看上面link的视频, CF的寿命从生后不久死亡增加到38岁了。不过, 国内CF经验不多。药也非常贵。